Progressive or Delayed Early-onset Pediatric Sensorineural Hearing Loss
نویسندگان
چکیده
منابع مشابه
Progressive cone dystrophy and sensorineural hearing loss.
A 39-year old man presented 13 years ago with a history of progressive loss of vision and photophobia. A full ophthalmological and ENT work-up during several years of follow-up, including psychophysical as well as electrophysiological tests, revealed a progressive cone dystrophy in combination with sensorineural hearing loss. His younger sister presented with very similar features and underwent...
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The association of ataxia, hypergonadotropic hypogonadism and hearing loss is extremely rare. Considerable heterogeneity exists in the literature of the neurological manifestations, age of onset, clinical severity and associated abnormalities. We describe a 24-year-old woman with secondary hypergonadotropic amenorrhea, early-onset progressive spinocerebellar ataxia (SCA), late-onset sensorineur...
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From the Department of Otolaryngology, University of British Columbia. Reprint requests: Neil S. Longridge, MD, 4th Floor, Willow Pavilion, Vancouver Hospital and Health Sciences Center, 805 West 12th Ave., Vancouver, B.C., Canada V5Z 1M9. Otolaryngol Head Neck Surg 1998;118:697-701. Copyright © 1998 by the American Academy of Otolaryngology– Head Neck Surgery Foundation, Inc. 0194-5998/98/$5.0...
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ژورنال
عنوان ژورنال: Nippon Jibiinkoka Gakkai Kaiho
سال: 2011
ISSN: 0030-6622,1883-0854
DOI: 10.3950/jibiinkoka.114.557